CASE REPORT OF A 17 - YEAR OLD GIRL WITH ATYPICAL CLINICAL PRESENTATION OF - ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY

Bojko Bjelaković, Goran Vukomanovic, Sanja Knežević Rangelov, Marko Jović

DOI Number
-
First page
63
Last page
66

Abstract


We report a case of a 17-year-old girl diagnosed with arrhythmogenic right ventricular cardiomyopathy (ARVC), who has been wrongly considered as having idiopathic ventricular extrasystoles for 13 years. The only noteworthy clinical finding until the final diagnosis was made, were complex ventricular arrhythmias (VA) during exercise as well as nonspecific repolarisations changes in inferolateral leads. We would like to increase paediatricians alertness to children presenting with so called “idiopathic” exercise induced VA that at time could turn out to be markers of arrhythmogenic condition.

Key words: arrhythmogenic right ventricular cardiomyopathy, ventricular arrhythmias

 


Full Text:

PDF

References


Romero J, Mejia-Lopez E, Manrique C, Lucariello R. Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC/D): A Systematic Literature Review. Clin Med Insights Cardiol [Internet]. 2013; 7:97-114. Available from: http://www.pubmedcentral.nih.gov/articlerender.fcgi?artid=3667685&tool=pmcentrez&rendertype=abstract

Yoo SJ, Grosse-Wortmann L, Hamilton RM. Magnetic resonance imaging assessment of arrhythmogenic right ventricular cardiomyopathy/dysplasia in children. Korean Circ J 2010; 40:357-367.

te Riele AS, Tandri H, Bluemke DA. Arrhythmogenic right ventricular cardiomyopathy (ARVC): cardiovascular magnetic resonance update. J Cardiovasc Magn Reson [Internet]. 2014; 16: 50.

Marcus FI, Zareba W. The electrocardiogram in right ventricular cardiomyopathy/dysplasia. How can the electrocardiogram assist in understanding the pathologic and functional changes of the heart in this disease? J Electrocardiol 2009; 42:136.

Gajewski KK, Saul JP. Sudden cardiac death in children and adolescents (excluding Sudden Infant Death Syndrome). Ann Pediatr Cardiol 2010; 3(2):107-112.

Dupuis JM, Tabib A, Reix P, Dupuis L, Daudet G, Jocteur-Monrozier D, et al. Sudden unexpected death of cardiac origin in the 6 to 18 years population. Pathologic data. Role of sports? How can we prevent it?. Arch Pediatr 2005; 12:1204-1208.

Asimaki A, Saffitz JE. The role of endomyocardial biopsy in ARVC: looking beyond histology in search of new diagnostic markers. J Cardiovasc Electrophysiol 2011; 22:111-117.

Bjelakovic B, Ilic S, Chouliaras K, Milovanovic B, Vukomanovic V, Bojic T, et al. Heart rate variability in children with exercise-induced idiopathic ventricular arrhythmias. Pediatr Cardiol 2010; 31:188-194.

Sun Y, Chan KL, Krishnan SM. Life-threatening ventricular arrhythmia recognition by nonlinear descriptor. Biomed Eng Online 2005; 4:6.

Kuo CS, Munakata K, Reddy CP, Surawicz B. Characteristics and possible mechanism of ventricular arrhythmia dependent on the dispersion of action potential durations. Circulation 1983; 67:1356-1367.

Nishikawa T, Ishiyama S, Sakomura Y, Nakazawa M, Momma K, Hiroe M, et al. Histopathologic aspects of endomyocardial biopsy in pediatric patients with idiopathic ventricular tachycardia. Pediatr Int 1999; 41:534-537.


Refbacks

  • There are currently no refbacks.


© University of Niš, Serbia
Creative Commons licence CC BY-NC-ND
ISSN 0354-4699 (Print)
ISSN 2406-050X (Online)