SURGICAL TREATMENT OF COMPLEX CROUZON SYNDROME CRANIOSYNOSTOSIS

Aleksandra Zdravkovic, Bojana Zivkovic, Mirko Micovic, Lukas Rasulic

DOI Number
https://doi.org/10.22190/FUMB181109014Z
First page
74
Last page
76

Abstract


Crouzon syndrome is one of the most common syndromic craniosynostosis. We present complex course of treatment in a child with Crouzon syndrome presented with multisuture craniosynostosis and hydrocephalus. A 3-months-old boy was admitted with clinical signs of hydrocephalus and turribrachycephaly. Firstly, the hydrocephalus was addressed. The ventriculoperitoneal shunt with programmable valve was implanted. Secondly, in May 2017, posterior calvarial remodeling was done. Finally, after the child recovered, anterior calvarial remodeling with fronto-orbital advancement was performed.  This completed the calvarial remodeling in this patient. Child is doing well, so far completing milestones of child development in time. This case presents an extremely complex case of syndromic multisuture craniosynostosis, in which it was necessary to perform the entire calvarial remodeling to correct the deformity and to provide a chance to the brain to grow and develop without constrictions.


Keywords

Crouzon syndrome, craniosynostosis, hydrocephalus, surgical treatment.

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References


Al-Namnam NM, Hariri F, Thong MK, Rahman ZA. Crouzon syndrome: Genetic and intervention review. J Oral BiolCraniofac Res. 2019,9:37-39.

Winn R. Youmans and Winn neurological surgery. 7th ed. 2017, Philadelphia, PA Elsevier.

Kalanjiam V, Manoharan GVMG. Crouzon syndrome – A rare case report. Int J Health Sci (Qassim). 2017, 11:74-75.

Balyen L, Deniz Balyen LS, Pasa S. Clinical characteristics of Crouzon syndrome. Oman J Ophthalmol. 2017, 10:120-122.

Cinalli G, Chumas P, Arnaud E, Sainte-Rose C. Renier D. Occipital Remodeling and Suboccipital Decompression in Severe Craniosynostosis Associated with Tonsilar Herniation. Neurosurg. 1998, 42:66-73.

Ong J, Harshbarger R, Kelley P, George T. Posterior Cranial Vault Distraction Osteogenesis: Evolution of Technique. SeminPlast Surg. 2014, 28:163–178.

Taylor JA, Bartlett SP. What’s New in Syndromic Craniosynostosis Surgery? Plastic and Reconstructive Surg.2017, 140:82e–93e.

Pijpers M, Poels PJ, Vaandrager JM, de Hoog M, van den Berg S, HoeveHJ, Joosten KFM. Undiagnosed obstructive sleep apnea syndrome in children with syndromalcraniofacial synostosis. J CraniofacSurg.2004, 15:670-4.

Heggie AA, Kumar R, Shand JM. The role of distraction osteogenesis in the management of craniofacial syndromes. Ann Maxillofac Surg. 2013, 3:4-10.

Thompson D, Jones B, Hayward R, Harkness W. Assessment and treatment of craniosynostosis. Br J Hosp Med. 1994, 52:17-24.

De Jong T, Bannink N, Bredero-Boelhouwer HH, van Veelen ML, Bartels MC, Hoeve LJ, Hoogeboom AJ, Wolvius EB, Lequin MH, van der Meulen JJ, van Adrichem LN, Vaandrager JM, Ongkosuwito EM, Joosten KF,Mathijssen IM. Long-term functional outcome in 167 patients with syndromiccraniosynostosis; defining a syndrome-specific risk profile. J PlastReconstrAesthet Surg. 2010, 63(10):1635-41.

Jeevan DS, Anlsow P,Jayamohan J. Abnormal venous drainage in syndromic craniosynostosis and the role of CT venography. Childs Nerv Syst. 2008, 24:1413-20.




DOI: https://doi.org/10.22190/FUMB181109014Z

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